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Above. Post-delivery anatomy. In hypoplastic left heart syndrome (HLHS), the left ventricle (LV) is hypoplastic (small and underdeveloped) and nonfunctional, while the right ventricle serves as the single pumping chamber. There is critical narrowing or absence of the mitral and/or aortic valves and hypoplasia of the ascending aorta and aortic arch.

Image courtesy: The Childrens’ Heart Clinic, PA, and Childrens’ Hospitals and Clinics of Minnesota.